Dr. PRABRISHA BANERJEE

DR. MD. SHAHID ALAM

Abstract

Cutaneous leiomyoma is a rarely occurring benign smooth muscle neoplasm of the skin. Piloleiomyoma, angioleiomyoma and genital leiomyoma are the three types of cutaneous leiomyoma. Piloleiomyoma, arising from the arrector pili muscle, is commonly found in the adult population. Congenital piloleiomyoma is extremely rare. It can be hereditary or sporadic. The involvement of eyelids in piloleiomyoma has never been reported before. We present a case of a neonate presenting with upper eyelid mass lesion since birth causing mechanical ptosis. An incisional biopsy followed by histopathology and immunohistochemistry confirmed the diagnosis of piloleiomyoma. There was associated cryptorchidism in our case, a systemic association that has never been reported. Cutaneous leiomyoma although, is a benign lesion, yet, it is associated with several systemic manifestations and malignancies. Hence, a detailed systemic evaluation is necessary for the management of cutaneous leiomyomas.