DR. AKULRAJ GUPTA

Dr.Preeti Rawat

Abstract

ONSMs are rare tumor in children.

Case Report: 10 year old female presented with complaints of protrusion of LE since 3 years which was progressive, painless and associated with diminution of vision. On examination her visual acuity was 6/9 in the RE and light perception in LE which has restriction of movement in all direction of gazes. Movement of RE was free and full. LE cornea has leucomatous opacity. The RE anterior segment and fundus were within normal limit. MRI showed diffusely enhancing lesion in left intraconal region around left optic nerve. Another Similar lesion measuring 12*12 mm noted on right side. LE enucleation was done because of severe proptosis and for right eye patient was referred to cancer hospital for fractionated radiation therapy

CONCLUSION: ONSMs should be included in the differential diagnosis of optic nerve tumor in children in spite of its rarity. If ONSMs occurs bilateral and is not promptly recognized, a total loss of vision may ensue.