Dr.Pushkar Dhir

Dr.Ronel Soibam, Dr. DIVA KANT MISRA, Dr.Awaneesh Upadhyay

Abstract

Persistent hyperplastic primary vitreous (PHPV) is an ocular developmental disorder resulting from incomplete apoptosis of the embryonic hyaloid vasculature. Unilateral PHPV is traditionally associated with a poor prognosis because of the challenges associated with managing progressive anisometropic amblyopia. Though the exact prevalence remains unknown, PHPV is considered to be not a very rare disease. The condition is usually unilateral and without associated systemic findings in normal full-term infants. A study on childhood blindness and visual loss in the United States showed that PHPV accounts for about 5 % of all cases of blindness.PHPV is usually divided into three types:Anterior,Posterior and Combined PHPV. Combined anterior and posterior PHPV is the most commonly seen clinical presentation.We present surgical management of 3 year male child with unilateral combined PHPV.